Rehabilitación neuropsicológica en personas con síndrome de Prader-Willi

Resumen

El síndrome de Prader-Willi (SPW) es un trastorno complejo del neurodesarrollo causado por anomalías genéticas y que presenta un fenotipo neuroconductual característico. El objetivo de este trabajo fue analizar las intervenciones de rehabilitación neuropsicológica en SPW, por lo que se realizó una búsqueda sistemática, incluyéndose un total de 14 artículos con intervenciones en características fenotípicas conductuales, cognitivas o familiares. Los estudios fueron analizados según el enfoque de la intervención, modelos, procedimientos específicos y resultados. La mayor parte de los estudios utilizaron un modelo de compensación y casi todos aplicaron técnicas de modificación conductual. Los resultados sugieren que las técnicas que utilizan un reforzamiento diferencial, que incluyen una mayor participación de la persona con SPW y sus familiares en el proceso de intervención, son más exitosas.
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Tapia De Moya, K. (2017). Rehabilitación neuropsicológica en personas con síndrome de Prader-Willi. Siglo Cero, 48(1), 73–93. https://doi.org/10.14201/scero2017487393

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Biografía del autor/a

Karol Tapia De Moya

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Universidad Autónoma de Madrid
Universidad Autónoma de Madrid. Oficina de acción solidaria y Cooperación. C/Einstein, 7. Campus de Cantoblanco. Edificio Plaza Mayor. Madrid
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