Rehabilitación neuropsicológica en personas con síndrome de Prader-Willi

Karol TAPIA DE MOYA

Resumen


El síndrome de Prader-Willi (SPW) es un trastorno complejo del neurodesarrollo causado por anomalías genéticas y que presenta un fenotipo neuroconductual característico. El objetivo de este trabajo fue analizar las intervenciones de rehabilitación neuropsicológica en SPW, por lo que se realizó una búsqueda sistemática, incluyéndose un total de 14 artículos con intervenciones en características fenotípicas conductuales, cognitivas o familiares. Los estudios fueron analizados según el enfoque de la intervención, modelos, procedimientos específicos y resultados. La mayor parte de los estudios utilizaron un modelo de compensación y casi todos aplicaron técnicas de modificación conductual. Los resultados sugieren que las técnicas que utilizan un reforzamiento diferencial, que incluyen una mayor participación de la persona con SPW y sus familiares en el proceso de intervención, son más exitosas.

Palabras clave


síndrome de Prader-Willi; fenotipo conductual; rehabilitación; neuropsicología.

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Referencias


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DOI: http://dx.doi.org/10.14201/scero2017487393

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